Duodenal atresia is the congenital absence or complete closure of a portion of the lumen of the duodenum. It causes increased levels of amniotic fluid during. Duodenal atresia or stenosis is a rare congenital digestive disorder that usually occurs for no apparent reason (sporadically). However, a few. A collection of disease information resources and questions answered by our Genetic and Rare Diseases Information Specialists for Duodenal atresia.

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Meanwhile, nutrition through a vein will be provided to the baby. The Center coordinator will keep you in contact with the appropriate physicians and specialists as well as coordinating the care for you and your baby after delivery. Anomalies associated with oesophageal atresia in Asians and Europeans. Your baby will be transferred to the Neonatal Unit soon after delivery. Early treatment includes removing fluids from the stomach via a nasogastric tubeand providing fluids intravenously.

The duodenum is the first portion of small intestine after the stomach that has many connections to and shares blood vessels with other organs such as the liver, gallbladder, and pancreas.

Choledochal cysts Caroli disease Biliary atresia. A few cases of duodenal atresia have been inherited as an autosomal recessive genetic trait. This will be discussed with you by the team caring for you during your pregnancy. To contact Children’s Memorial Hermann Hospital, please fill out the form below.

The mother’s amniotic fluid and the growth of the baby will be monitored closely with ultrasound by the obstetrician. Adzlah signs and symptoms of adult pyloric stenosis are similar to those in the infant. The Johns Hopkins University. Very occasionally it maybe necessary for your baby to have another X-ray to confirm the diagnosis.


Duodenal Atresia or Stenosis – NORD (National Organization for Rare Disorders)

This may have been detected on an antenatal scan or may not be detected until after the delivery when the baby starts to vomit. After birth, duodenal atresia may cause abdominal distension, especially of the upper abdomen. Duodenal atresias can occur as atreeia complete or partial blockage of any portion of the duodenum.

The Center team will help care for you and your infant with duodenal atresia.

When the atresia is located in the first part of the duodenum, a gastrojejunostomy may be the treatment of choice. Duodenal atresia may be recognized through ultrasound by the presence of a “double bubble” which can be seen in the abdominal area. This page was last edited on 14 Octoberat The appearance of this condition resembles a Christmas tree or apple peel when viewed by a surgeon. The baby will receive all of the calories necessary to grow until he or she can be fed through the intestinal tract.

This information regarding your condition is meant to be a helpful, informative introduction. This abnormality causes a portion of the small intestine the jejunal to twist around one of the arteries of the colon. Long lines and central lines. This is a procedure in which a connection is formed between the duodenum and the jejunum.

Because too little food reaches the intestines, constipation is a frequent complication, as is failure of the infant to gain weight. It causes increased levels of amniotic fluid during pregnancy polyhydramnios and intestinal obstruction in newborn babies.

Duodenal atresia

However, a few cases of duodenal atresia have been inherited as an autosomal recessive genetic trait. Once bowel function returns, it will take a period of time before he or she stresia handle enough formula or breast milk to provide full nutrition. Newborns with duodenal atresia will need an operation in order to fix the intestinal atresia.


An X-ray of the abdomen shows two large air filled spaces, the so-called “double bubble” sign. Because the amniotic fluid is normally swallowed and digested by the fetus, duodenal atresia can cause an increase in fluid in the amniotic sac, hydramnios. Severe hydramnios may put doudenum mother at risk for early delivery.

Symptoms of partial duodenal blockage vary depending on the severity.

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Newborns diagnosed with duodenal atresia often present with vomiting. Prenatal diagnosis is usually based on non-specific signs on fetal ultrasound such as a dilated stomach. Gastrointestinal tract disorders Congenital disorders of digestive system.

Sometimes this can be much longer, depending on the degree of prematurity and the condition of the bowel.

The majority of cases of duodenal atresia or stenosis occur for no apparent reason sporadically. Twenty-five percent of their children may receive both normal genes, one from each parent, and will be genetically normal for that particular trait.

The earlier the disorder is recognized and surgery is performed, the better the outcome. Pyloric stenosis Hiatus hernia. The fetal team will closely evaluate your fetus with duodenal atresia and help determine the best course of treatment. This line is usually placed in a small vein in an arm or leg and fed through into a large vein.